Connolly MJ, et al. - The purpose of this study is to test whether CT signs of PVOD (CTS-PVOD) were frequent in SSc-PAH and whether they were related to pulmonary oedema on therapy and worse survival. The outcome of this study revealed that the CTS-PVOD were less frequent in this SSc-PAH cohort than in previous reports but the presence of not less than two of these signs is related to pulmonary oedema on therapy and a trend towards worse survival on univariate examination.