Young NM, et al. – This review outlined the perioperative complications, benefits, and the timeframe over which auditory skills develop in children with CHARGE syndrome after cochlear implantation (CI). Findings suggested that auditory skills might develop slowly after CI in children with CHARGE syndrome but most could achieve at least improved detection. In this study cohort, half acquired some speech perception ability. Cochlear nerve deficiency was frequent, but should not be a contraindication to implantation.