Shao K, et al. - Given that clinicopathological features, standard treatment methods and prognosis of the pulmonary ciliated muconodular papillary tumor (CMPT) has not been well defined, researchers performed a retrospective analysis of two cases of CMPT diagnosed and treated in their hospital and 39 cases reported in the published literature. The cohort thus comprised 41 CMPT patients including 20 males and 21 females (aged 9–84 years). The primary tumor had a diameter of 0.3–4.5 cm. As observed on computed tomography, these lesions were mostly subsolid nodules, and were easily misdiagnosed as early lung adenocarcinoma. Accurate diagnosis of CMPT could be made via performing immunohistochemistry. Mutations in EGFR, KRAS, and BRAF and ALK rearrangements in CMPT were reported in gene alternation studies. Surgical treatment was undertaken in all the patients with no receipt of postoperative adjuvant therapy. During the follow-up duration of 0–120 months, they identified no case of tumor recurrence. These findings suggest a low incidence of CMPT with a high rate of image misdiagnosis. Sub-lobectomy may be proper and adjuvant treatment should be avoided since the disease is now prone to benign lesions.